Malignant Peripheral Nerve Sheath Tumour of Small Intestine, an Unusual Tumour: A Case Report and Review of the Literature Parvathi Metta1, Rao Konkena Janardhana2,**, Rao Gunta Santa3a,3b,***, Srinubabu Kollu4,****, Neelam Prasad4,* 1Assistant Professor, Department of Dermatology Venereology and Leprology, Andhra Medical College, Visakhapatnam, Andhra Pradesh, India 2Assistant Professor, Department of General Surgery, King George Hospital, Visakhapatnam, Andhra Pradesh, India 3aProfessor and Head, Director of Medical Education, Andhra Pradesh, Hyderabad, India 3bDepartment of General Surgery, Andhra Medical College, Visakhapatnam 4PG Student, Department of General Surgery, Andhra Medical College, Visakhapatnam, Andhra Pradesh, India *Corresponding author email id: prasadneelam04@gmailcom, prasadneelam04@yahoo.co.in
**kjrvskp@gmail.com
***dr.santarao@yahoo.com
****srinubabupond@gmail.com
Online published on 11 November, 2014. Abstract Neurofibromatosis type-1 (NF1), also known as von Recklinghausen disease, is a common autosomal dominant condition. It is a multisystem disorder. Abdominal involvement in patients with NF1 has been described in the form of neurofibromas within the liver, mesentery, retroperitoneum and gastrointestinal (GI) tract. Involvement of bowel is rarely seen. Malignant peripheral nerve sheath tumour of small intestine is a rare entity with very few cases reported in literature. Surgery remains the only curative option. Chemotherapy may be used as an adjuvant for advanced diseases. We report a case of malignant peripheral nerve sheath tumour of small intestine which presented as acute intestinal obstruction. Top Keywords Neurofibromatosis type-1(NF1), Malignant peripheral nerve sheath tumour, Acute intestinal obstruction. Top |